Abdominal wall defects – gastroschisis, omphalocele

Česká verzia

Authors: E. Orlová ¹; M. Brejchová ²; B. Kučerová ³
Authors place of work: Novorozenecké oddělení s JIRP, FN Motol, Praha ¹; Gynekologicko-porodnická klinika 2. LF UK a FN Motol, Praha ²; Klinika dětské chirurgie 2. LF UK a FN Motol, Praha ³
Published in the journal: Čes-slov Neonat 2024; 30 (1): 19-24.
Category: Reviews

Summary

Abdominal wall defects are some of the most common congenital anomalies met in the pediatric population. These defects include two separate pathologies: gastroschisis and omphalocele, which have divergent pathophysiologic origins, clinical manifestations, and management strategies. Both are usually diagnosed prenatally using fetal ultrasonography, and affected patients should be treated at centers with access to high-risk obstetric, neonatology and pediatric surgery services. Delivery outside a perinatal center is a significant predictor of complications for infants born with gastroschisis. Choosing the most suitable surgical technique, with detailed postoperative monitoring of the patient, is particularly important due to the risk of possible abdominal compartment syndrome. Overall, the long-term outcome and survival for these patients is good and the results of patients in Czech Republic are comparable to most developed countries in the world. In this review, we discuss the distinguishing features, current management strategies, and outcomes of patients with these defects.

Keywords:

gastroschisis – omphalocele – intra-abdominal pressure – abdominal compartment syndrome

Zdroje

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Konflikt zájmu: žádný. Došlo do redakce: 5. 3. 2024

Adresa pro korespondenci:
MUDr. Ekaterina Orlová
Novorozenecké oddělení s JIRP
Gynekologicko-porodnická klinika 2. LF UK a FN Motol
V Úvalu 84
150 06 Praha 5
e-mail: ekaterina.orlova@fnmotol.cz