About Cryptophthalmos
(2^nd Czech Study)

Česká verzia

Authors: J. Krásný ¹; M. Čakrtová ²; J. Kletenský ²; Novák V. (+) ³; J. Šach ⁴
Authors place of work: Oční klinika FN Královské Vinohrady, Praha, přednosta prof. MUDr. P. Kuchynka, CSc. ¹; Klinika plastické chirurgie FN Královské Vinohrady, Praha přednosta doc. MUDr. M. Tvrdek, CSc. ²; Katedra polymerů, Vysoká škola chemicko-technologická, Praha vedoucí doc. ing. V. Schätz, CSc., (+) a prof. Ing. V. Dudáček, DrSc. ³; Ústav patologické anatomie FN Královské Vinohrady a 3. LF UK, Praha vedoucí prof. MUDr. V. Mandys, DrSc. ⁴
Published in the journal: Čes. a slov. Oftal., 71, 2015, No. 6, p. 278-286
Category: Original Article

Předneseno na IX. a XI. sympoziu dětské oftalmologie, Litomyšl 2009 a Olomouc 2013
Věnováno památce doc. MUDr. J. Otradovce, CSc., zakladateli moderní české orbitologie

Summary

Aim:
To get acquainted with the 2^nd Czech study about cryptophthamos and with self-surgical methods.

Material:
The boy with unilateral complete cryptophthalmos of left eye was treated from 2 to 20 years. The girls was treated from 4 month to 5 year yet for right abortive cryptophthalmos with microblepharon and left complete type still waiting for solutions.

Surgical methods and results:
Authors present a surgical procedures for correction of the upper and lower eyelids and ocular anomalies both patients studied. Successful reconstruction of palpebral fissure took place in several stages at the boy. The surgical procedure gradually contained: the insertion of gradually increased convex concave circular-shaped implant (silicone ruber) due a modeling of palpebral fissure, an enucleation of rudimentary eye, a reconstruction of bottom palpebral fissure by retro-auricular skin graf and a releasing of the lower transitory fold by the cul-de-sac method. An adequate depth of palpebral fissure to allow perfect position of an aesthetic protesis. Enucleated eye was atypically shaped, remiding partly sand-glass clock. The cornea was replaced by thick fibrous membrane, the iris and the lens were not revealed. Gliomatic retina was detached nearly totaly and the optic nerv was rudimental. The repairing the upper lid coloboma of girl by a lid rotation flap reconstruction using the inferior eyelid was performed at the age 17 month. Corneal dermoid simultaneously removed (histologically verified). Upper conjunctival fornix was formed using the spherical covering foil (silicone rubber) before and after the reconstruction of the lid.

Conclusions:
Plastic reconstructions required the need for patient access without trying immediate effect. An important role played silicone rubber implants (elastomer medical grade) which used temporarily.

Key words:
cryptophthalmos, microblepharon, relief surgery, silicon ruber implants

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