Pregnancy in women with congenital bleeding disorder

Česká verzia

Authors: T. Binder ¹; P. Salaj ²; V. Komrska ³
Authors place of work: Gynekologicko-porodnická klinika FZS UJEP a MN, Ústí nad Labem, přednosta doc. MUDr. T. Binder, CSc. ¹; ÚHKT, Praha, přednosta prof. MUDr. P. Cetkovský, Ph. D., MBA ²; Dětská hemato-onkologická klinika 2. LF UK a FN Motol, Praha, přednosta prof. MUDr. J. Starý, DrSc. ³
Published in the journal: Ceska Gynekol 2016; 81(6): 420-425

Summary

The aim of the study:
To highlight the risks associated with pregnancy at women with von Willebrand´s disease or hemophilia. Introduce the rules of multidisciplinary prenatal and peripartal care to minimalize these risks. The article is accompanied by case report where maladministration led to fatal consequences for the newborn.

Design:
Review and case report.

Seatings:
Department Obstetric and Gynecology UJEP and Masaryk´s Hospital Ústí n/Labem, Institute Haematology and Blood Transfer Prague, Children´s Haemato-onkology Clinic University Hospital Prague Motol.

Coclusions:
The pregnancy in both above-mentioned diseases is risky. The close multidisciplinary collaboration is required.

Keywords:
pregnancy, von Willebrad´s disease, hemophilia

Zdroje

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3. Chee, YL., Townend, J., Crowther, M., et al. Assessment of von Willebrand disease as a risk factor for primary postpartum haemorrhage. Haemophilia, 2012, 18, p. 593–597.

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