Quality of Life in Patients with Epidermolysis Bullosa
Authors:
J. Kýrová; H. Bučková
Authors place of work:
Dětské kožní oddělení Pediatrické kliniky, FN Brno a LF MU Brno
primářka MUDr. Hana Bučková, Ph. D.
Published in the journal:
Čes-slov Derm, 88, 2013, No. 3, p. 123-127
Category:
Clinical and laboratory Research
Summary
Skin disease can have a profound impact on many aspects of daily life, especially when affecting visible parts of the body. Pain, itch, odour and time-consuming dressings are problems influencing self-confidence, personal relationship, education and employment in patients with epidermolysis bullosa congenita.
Standardised questionnaires are useful tools for assessing the impact of disease on quality of life (QL). The aim of the authors was to assess the impact of epidermolysis bullosa on QL of patients treated in EB Centre Czech Republic in the period 2009–2010. Dermatology Life Quality Index (DLQI) and Children’s Dermatology Life Quality Index (CDLQI) questionnaires were used in the survey. Total of 43 patients (27 children and 16 adults) were included. More than one third of both children and adult patients stated large or very large impact on QL. The most serious impact on QL was found in patients with recesive dystrophic EB and in children with generalized form of simplex EB. On the other hand, patients with dominant dystrophic EB in both age groups indicated the lowest impact on QL.
Key words:
epidermolysis bullosa – quality of life – Dermatology life quality index – Children’s dermatology life quality index
Zdroje
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Štítky
Dermatology & STDs Paediatric dermatology & STDsČlánok vyšiel v časopise
Czech-Slovak Dermatology
2013 Číslo 3
Najčítanejšie v tomto čísle
- Atypical Melanocytic Lesions
- Bullous Pemphigoid Induced by Vaccination
- Quality of Life in Patients with Epidermolysis Bullosa