Congenital Dermatofibrosarcoma Protuberans
Authors:
Z. Plzáková 1; M. Důra 1,2; P. Dundr 1,2; J. Štork 1
Authors place of work:
Dermatovenerologická klinika 1. LF UK a VFN, Praha
přednosta prof. MUDr. J. Štork, CSc.
1; Ústav patologie 1. LF UK a VFN, Praha
přednosta doc. MUDr. P. Dundr, Ph. D.
2
Published in the journal:
Čes-slov Derm, 91, 2016, No. 1, p. 18-21
Category:
Case interpretation
Summary
Dermatofibrosarcoma protuberans is a slowly growing skin tumor of low malignant potential and high local recurrence rate. It appears in adults, infantile and congenital forms are rare and their diagnosis is often delayed. We present a case of 32-year-old female with congenital tumour and discuss its differential diagnosis and therapeutic possibilities.
Key words:
dermatofibrosarcoma protuberans – congenital dermatofibrosarcoma protuberans – differential diagnosis – wide local excision – imatinib mesylate
Zdroje
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Štítky
Dermatology & STDs Paediatric dermatology & STDsČlánok vyšiel v časopise
Czech-Slovak Dermatology
2016 Číslo 1
Najčítanejšie v tomto čísle
- Hereditary Ichthyoses
- Congenital Dermatofibrosarcoma Protuberans
- Psoriasis, Psoriatic Arthritis and Tophaceous Gout