Primary pulmonary hemosiderosis – experiences from Banska Bystrica

Česká verzia

Authors: I. Gondová ^1,2; B. Takáč ¹; E. Bubanská ³; S. Dluholucký ^1,4; K. Králinský ^1,4; K. Novotná ⁵; J. Koňarčík ⁶; M. Ducár ⁶
Authors place of work: II. Detská klinika SZU, DFNsP, Banská Bystrica, Slovensko ¹; Vysoká škola zdravotníctva a sociálnej práce sv. Alžbety, Bratislava, Slovensko ²; Klinika pediatrickej onkológie a hematológie SZU a DFNsP, Banská Bystrica, Slovensko ³; Fakulta zdravotníctva, Slovenská zdravotnícka univerzita, Banská Bystrica, Slovensko ⁴; Oddelenie rádiológie FNsP FDR, Banská Bystrica, Slovensko ⁵; Martinské bioptické centrum, s. r. o, Banská Bystrica, Slovensko ⁶
Published in the journal: Čes-slov Pediat 2019; 74 (3): 176-181.
Category: Case Report

Summary

Idiopathic pulmonary hemosiderosis is rare inetersticial lung disease, the incidence is 6.3 children on million of childhood patients in Slovak Republic. It is chronic disease with period of relapse and remission. The ethiology is not clear, probably the immune system is dysfunctional, indicating the autoimmune origin of the disease. Diagnosis is based on combination of reccurent hemoptysis , anemia in laboratory samples, pulmonary infiltrates on chest X-ray. Due to late diagnosis and progression, the prognosis is not favorable.

Since the establishment of our hospital, there have been two cases of idiopathic pulmonary hemosiderosis. The first one in 2004, in treatment was used human recombinant erytropoetin. The second one ocuured
13 years later – in 2017.

In the next article approach the authors the two case studies. Has ist changed something in the view of hemosiderosis over the past period?

Keywords:

idiopathic pulmonary hemosiderosis – anemia

Zdroje

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