NEPHROBLASTOMA – CURRENT EVALUATION AND TREATMENT

Česká verzia

Authors: Marcela Pýchová ¹; Karel Švojgr ²; Josef Mališ ²; Michal Rygl ¹; Karel Pýcha ¹; Martin Kynčl ³; Roman Kodet ⁴; Jan Starý ²; Jiří Šnajdauf ¹
Authors place of work: Klinika dětské chirurgie 2. LF UK a FN Motol, Praha ¹; Klinika dětské hematoonkologie 2. LF UK a FN Motol, Praha ²; Klinika zobrazovacích metod 2. LF UK a FN Motol, Praha ³; Ústav patologie a molekulární medicíny 2. LF UK a FN Motol, Praha ⁴
Published in the journal: Ces Urol 2016; 20(2): 113-122
Category: Review article

Summary

Nephroblastoma (Wilms tumor – WT) is the most common solid renal tumor in children. The patients are treated according to SIOP 2001 protocol. This protocol recommends pre-operative chemotherapy, nephrectomy and postoperative treatment. Blastemal and anaplastic histological subtypes are poor prognostic factors. It is a well treatable disease, with up to 90 % of patients cured.

Key words:
Nephroblastoma, therapy, Wilms´ tumor.

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