Isolated ventricular non-compaction: review article with a case-report example

Česká verzia

Authors: Karel Vondrák
Authors place of work: Kardiocentrum, III. interní kardiologická klinika 3. LF UK a FN Královské Vinohrady, Praha, přednosta prof. MUDr. Petr Widimský, DrSc., FESC, FACC
Published in the journal: Vnitř Lék 2014; 60(2): 164-170
Category: Case Report

Summary

Isolated ventricular non-compaction (IVNC) is rare, genetically determined disorder characterized by prominent trabecularization of luminal side of the ventricular wall with deep recesses. The disease is believed to arise due to an in utero arrest of the compaction of the former loose meshwork of myocardial trabeculations. The symptoms of the disease include: heart failure, thromboembolic complications and arrhythmias. The course of the disease is variable ranging from patients with IVNC diagnosis as an incidental finding, to cases of severe heart failure and sudden cardiac death. This article brings an overview of the current state of knowledge on the disease and finally presents a short case-report of patient with IVNC.

Key words:
arrhythmias – echocardiography – heart failure – thromboembolic complications – ventricular non-compaction

Zdroje

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