Early diagnosis of systemic scleroderma

Česká verzia

Authors: Adéla Skoumalová ¹; Pavel Horák ¹; Zuzana Heřmanová ²; Jakub Videman ¹; Andrea Smržová ¹; Viktor Palla ³
Authors place of work: III. interní klinika – nefrologická, revmatologická a endokrinologická, FN a LF UP Olomouc ¹; Ústav imunologie, FN a LF UP Olomouc ²; Klinika chorob kožních a pohlavních, FN a LF UP Olomouc ³
Published in the journal: Vnitř Lék 2022; 68(5): 285-289
Category: Main Topic
doi: https://doi.org/10.36290/vnl.2022.061

Summary

Systemic scleroderma (SSc) is a systemic immune-mediated connective tissue disease characterized by fibroproductive changes in connective tissue and microvascular disorders. The disease affects the skin, musculoskeletal system and internal organs. It is a disease with a significant rate of morbidity and mortality, significantly worsening the quality of life of patients. Early initiation of therapy is necessary to prevent disease progression. This review article discusses the current possibilities of early diagnosis of systemic scleroderma.

Keywords:

diagnostics – early forms of scleroderma – systemic scleroderma

Zdroje

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