Surgical Treatment of Extensive Fibrous Dysplasia in the Craniofacial Region – a Case Report

Česká verzia

Authors: F. Kurinec ¹; B. Rudinský ²; L. Marinčák ³
Authors place of work: Otorinolaryngologická klinika FNsP Nové Zámky ¹; Neurochirurgická klinika FNsP Nové Zámky ²; CEIT Biomedical Engineering, s. r. o., Košice ³
Published in the journal: Cesk Slov Neurol N 2016; 79/112(6): 723-727
Category: Kazuistika

Summary

Fibrous dysplasia is a rare non-malignant bone disorder. The bone affected by this disorder is replaced by abnormal fibrous connective tissue. This normal fibrous tissue weakens the bone, making it abnormally fragile and prone to a fracture. Fibrous dysplasia may affect one solitary bone (monoostotic disease) or the disorder can be widespread, affecting multiple bones (polyostotic disease). Fibrous dysplasia is usually diagnosed in children or young adults but mild cases may go undiagnosed until adulthood. The case report describes management and surgical treatment of extensive fibrous dysplasia in a 29-year-old man.

Key words:
fibrous dysplasia – craniofacial – surgical treatment

The authors declare they have no potential conflicts of interest concerning drugs, products, or services used in the study.

The Editorial Board declares that the manuscript met the ICMJE “uniform requirements” for biomedical papers.

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