Vein of Galen congenital malformation in newborn

Česká verzia

Authors: H. Kolarovszká ¹; L. Časnocha Lúčanová ¹; K. Zeleňák ³; R. Richterová ²; M. Kozár ¹ ; K. Maťašová ¹
Authors place of work: Neonatologická klinika, Jesseniova lekárska fakulta v Martine, Univerzita Komenského v Bratislave Univerzitná nemocnica Martin prednosta prof. MUDr. M. Zibolen, CSc. ¹; Neurochirurgická klinika, Jesseniova lekárska fakulta v Martine, Univerzita Komenského v Bratislave, Univerzitná nemocnica Martin prednosta doc. MUDr. B. Kolarovszki, PhD. ²; Rádiologická klinika, Jesseniova lekárska fakulta v Martine, Univerzita Komenského v Bratislave Univerzitná nemocnica Martin prednosta doc. MUDr. K. Zeleňák, PhD. ³
Published in the journal: Čes-slov Pediat 2016; 71 (5-6): 275-280.
Category: Kazuistika

Summary

Vein of Galen aneurysmal malformation is rare vascular developmental anomaly that arises prenataly and is ussually diagnosed during prenatal sonographic screening investigation or just in neonatal period. Ethiopathogenic factors of the disease are not well known and clinical features are various. Prenataly, congenital disease can be presented as cardiac failure or fetal hydrops. Postnatal clinical picture is usually asymptomatic and vascular anomaly is found during screening sonographic investigation of the brain or it is manifested as cardiac insufficiency in varying degrees. An important part of patient management is a multidisciplinary approach that allows early diagnosis of the disease, which is a prerequisite for successful treatment.

Authors present two case reports of newborns with different clinical manifestation and management in early postnatal period.

Key words:
newborn, vascular anomaly, vein of Galen

Zdroje

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