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Carcinoid of the Appendix Goblet Cells Metastasize to the Orbit – a Clinical Case Report and Review of the Literature


Authors: V. M. Matějka 1;  P. Mukenšnabl 2;  R. Tupý 3;  O. Fiala 1;  J. Fínek 1
Authors place of work: Onkologická a radioterapeutická klinika LF UK a FN Plzeň 1;  Šiklův ústav patologie, LF UK a FN Plzeň 2;  Klinika zobrazovacích metod LF UK a FN Plz 3
Published in the journal: Klin Onkol 2016; 29(3): 220-223
Category: Case Reports
doi: https://doi.org/10.14735/amko2016220

Summary

Goblet cell carcinoid (GCC) of the appendix is extremely rare, representing approximately 5% of all primary appendiceal neoplasms. Histologically there are three groups of GCC: group A (typical GCC), adenocarcinoma ex GCC signet ring cell type (group B), and adenocarcinoma ex GCC poorly differentiated carcinoma type (group C), which is the most aggressive. GCC metastasizes in 15–60% of cases, mainly to the ovaries, pelvis, abdominal cavity, ribs, vertebrae, and lymph nodes. Hematogenous metastasis to the liver or other parenchymal organs can occur, but this is very rare. The different organs metastases haven’t been described yet. The primary mode of treatment is radical surgical resection or debulking, followed by chemotherapy; however, patients with unresectable or recurrent GCC are candidates for systemic therapy. Here, we report a case of very aggressive GCC of the appendix, which had metastazed to the liver at the time of diagnosis and subsequently metastasized to the orbit.

Key words:
carcinoid tumor –  goblet cells –  metastatic –  appendix –  orbit

The authors declare they have no potential conflicts of interest concerning drugs, products, or services used in the study.

The Editorial Board declares that the manuscript met the ICMJE recommendation for biomedical papers.

Submitted:
2. 2. 2016

Accepted:
25. 4. 2016


Zdroje

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3. Anderson NH, Somerville JE, Johnston CF et al. Appendiceal goblet cell carcinoids: a clinicopathological and immunohistochemical study. Histopathology 1991; 18(1): 61– 65.

4. Tang LH, Shia J, Soslow RA et al. Pathologic classification and clinical behavior of the spectrum of goblet cell carcinoid tumors of the appendix. Am J Surg Pathol 2008; 32(10): 1429– 1443.

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7. Roy P, Chetty R. Goblet cell carcinoid tumors of the appendix: an overview. World J Gastrointest Oncol 2010; 2(6): 251– 258. doi: 10.4251/ wjgo.v2.i6.251.

8. Stancu M, Wu TT, Wallace C et al. Genetic alterations in goblet cell carcinoids of the vermiform appendix and comparison with gastrointestinal carcinoid tumors. Mod Pathol 2003; 16(12): 1189– 1198.

9. Pham TH, Wolff B, Abraham SC et al. Surgical and chemotherapy treatment outcomes of goblet cell carcinoid: a tertiary cancer center experience. Ann Surg Oncol 2006; 13(3): 370– 376.

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Štítky
Paediatric clinical oncology Surgery Clinical oncology

Článok vyšiel v časopise

Clinical Oncology

Číslo 3

2016 Číslo 3
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