Extreme Hypertrophy of Peripheral Neuronal Structures in CIDP – a Case Study

Česká verzia

Authors: J. Michalik ¹; E. Kurča ¹; M. Hladká ²; B. Hofericová ¹; V. Nosáľ ¹; M. Grofik ¹; E. Kantorová ¹; M. Adámková ¹
Authors place of work: JLF UK a UN Martin Neurologická klinika ¹; JLF UK a UN Martin Rádiologická klinika ²
Published in the journal: Cesk Slov Neurol N 2011; 74/107(1): 72-75
Category: Case Report

Summary

Chronic inflammatory demyelinating polyradiculoneuropathy (CIDP) is an autoimmune peripheral nerve disease characterized by flaccid quadriparesis with loss of sensitivity and possible damage to cranial nerves. The diagnosis of CIDP nay involve electromyography (EMG), cerebrospinal fluid analysis, nerve biopsy, magnetic resonance imaging (MRI) of peripheral nerves and the clinical response to immunosuppression and/or immunomodulation. MRI facilitates early detection of nerve hypertrophy. In our case report we present an unusual CIDP with extreme hypertrophy of the peripheral nerves and spinal roots.

Key words:
chronic inflammatory demyelinating polyradiculoneuropathy – hypertrophy – magnetic resonance imaging

Zdroje

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