Malignant Peripheral Nerve Sheath Tumour of Cervical Plexus – a Case Report

Česká verzia

Authors: Z. Kadaňka Jr ¹; J. Hanák ²; B. Gál ²
Authors place of work: Neurologická klinika LF MU a FN Brno ¹; ORL klinika LF MU a FN u sv. Anny v Brně ²
Published in the journal: Cesk Slov Neurol N 2013; 76/109(6): 751-755
Category: Case Report

Summary

Malignant peripheral nerve sheath tumours are rare neoplasms, especially in the head and neck. They are often asymptomatic. We present a case of 29-years old patient with neurofibromatosis type 1 with malignant tumour of the cervical plexus. A small resistance in the upper mediastinum was diagnosed (ganglioneurinoma) in 2005 and treated surgically (total exstirpation). A small infiltration in the right supraclavicular area occurred five years later and was also managed surgically (debulking) – histologically MPNST. There was a relapse of this tumour in the same area in 2011; this was treated by en bloc resection, followed by chemotheraphy. At present, the patient is in a good clinical status, with no neurological deficit.

Key words:
malignant peripheral nerve sheath tumour – cervical plexus – malignant schwannoma – neurofibromatosis type 1

The authors declare they have no potential conflicts of interest concerning drugs, products, or services used in the study.

The Editorial Board declares that the manuscript met the ICMJE “uniform requirements” for biomedical papers.

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