Diastematomyelia in Adults – a Case Report

Česká verzia

Authors: V. Novák; L. Hrabálek; M. Vaverka; M. Halaj
Authors place of work: Neurochirurgická klinika LF UP a FN Olomouc
Published in the journal: Cesk Slov Neurol N 2015; 78/111(4): 486-489
Category: Case Report

Summary

Diastematomyelia is a rare congenital defect, a type of spinal dysraphisms, often associated with the tethered cord syndrome. Diastematomyelia is formed by the two halves of the split spinal cord that each has own dural sac separated by a rigid or fibrotic septum. This defect is mainly diagnosed in children. Pain is the dominant symptom in adult patients. The authors present a case of a woman aged 44 years with diastematomyelia who complained of chronic back pain and progressive weakness in her legs. In this patient, laminectomy was performed, the spinal cord released and the dural sac restored. After the surgery, the patient had no neurological deficits and reported significant pain relief.

Key words:
diastematomyelia in adults – tethered cord syndrom – split cord malformation

The authors declare they have no potential conflicts of interest concerning drugs, products, or services used in the study.

The Editorial Board declares that the manuscript met the ICMJE “uniform requirements” for biomedical papers.

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