Lymphangiomatosis – very rare disease of the lymphatic vessels
Authors:
Zdeněk Král 1; Marta Krejčí 1; Ivana Červinková 2; Luděk Pour 1; Martin Štork; Martin Krejčí 1; Viera Sandecká 1; Zdeněk Adam 1
Authors place of work:
Interní hematologická a onkologická klinika LF MU a FN Brno
1; Klinika dětské radiologie LF MU a FN Brno
2
Published in the journal:
Vnitř Lék 2021; 67(E-4): 9-12
Category:
Review Articles
Summary
Lymphangiomatosis is rare disease, we can find this entity in differential diagnosis of osteolytic leasions of bones of unknown origin. Typical sign for lymphangiomatosis is proliferation of lymphatic tissue with production of lymphangiomas in various organs and systems. Clinical manifestation of disease is variable, involvement of lungs and bone is typical. In our article we present recent classification of lymphatic tissue neoplasias, their clinical symptoms and treatment possibilities.
Keywords:
lymphangiomatosis
Zdroje
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Štítky
Diabetology Endocrinology Internal medicineČlánok vyšiel v časopise
Internal Medicine
2021 Číslo E-4
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