Cogan's Syndrome

Česká verzia

Authors: D. Jančatová ¹; Pavel Komínek ^1,2 ; Karol Zeleník ^1,2
Authors place of work: Otorinolaryngologická klinika FN Ostrava, přednosta prof. MUDr. P. Komínek, Ph. D, MBA ¹; Lékařská fakulta, Ostravská univerzita ²
Published in the journal: Otorinolaryngol Foniatr, 64, 2015, No. 1, pp. 42-45.
Category: Case Reports

Summary

Cogan's Syndrome a case of a 20-year-old woman with Cogan syndrome. Cogan's syndrome is a rare chronic vasculitis, in its typical form characterized by progressive sensorineural hearing loss, vestibular symptoms resembling Menière’s disease and non-syphilitic interstitial keratitis. The interval between the onset of audiovestibular and ocular symptoms varies in the range of 1–6 months. This syndrome primary affects young adults, without sexual predominance, the peak of the incidence is between 20 and 30 years of age. Till now less than 250 cases have been reported, in one half ot the cases the disease leads to definitive deafness. There are no diagnostic criteria for Cogan's syndrome, only the typical clinical presentation (combination of inflammatory eye disease, vestibular dysfunction and progressive hearing loss). Early diagnosis and treatment is crucial for the prognosis of the patients.

Keywords:
Cogan's syndrome, typical and atypical form, hearing loss, vestibular symptoms, interstitial keratitis, corticotherapy, immunosuppression

Zdroje

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