Ňaršanská A., Třeška V., Mírka H., Mukenšnabl P., Chlumská A.: Caroli Disease – Dilatation of Intrahepatic Bile Ducts

Česká verzia

Authors: A. Ňaršanská; V. Třeška; H. Mírka ¹; P. Mukenšnabl ²; A. Chlumská ²
Authors place of work: Chirurgická klinika FN a LF UK v Plzni, přednosta: prof. MUDr. Vladislav Třeška, DrSc. ; Radiodiagnostická klinika FN a LF UK v Plzni, přednosta: doc. MUDr. Boris Kreuzberg, CSc. ¹; Šiklův patologicko-anatomický ústav FN a LF UK v Plzni, přednosta: prof. MUDr. Michal Michal, Ph. D. ²
Published in the journal: Rozhl. Chir., 2011, roč. 90, č. 5, s. 281-284.
Category: Monothematic special - Original

Summary

Caroli disease is a rare congenital condition characterized by a non-obstructive saccular or fusiform multi-focal segmental dilatation of the intrahepatic bile ducts and the frequent formation of the intrahepatic calculi. It can affect the entire liver with manifestations in the childhood, or only some segments, which may be an asymptomatic condition found accidentally in the adulthood. In other cases, the condition is manifested primarily with tract infections. The authors of the three case reports describe pitafalls of the diagnosis and treatment of the segmental Caroli disease, which is manifested in the adulthood. The treatment was a resection of the affected liver segments.

Key words:
Caroli disease – dilatation of the intrahepatic bile – surgery treatment

Zdroje

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