Wunderlich‘s syndrome in patient with sporadic bilateral angiomyolipomas – case report

Česká verzia

Authors: H. Shaikh ¹; B. Nechanská ²
Authors place of work: Urologické oddělení, Oblastní nemocnice Kladno, a. s. ¹; Urologické oddělení, Oblastní nemocnice Mladá Boleslav, a. s. ²
Published in the journal: Rozhl. Chir., 2020, roč. 99, č. 12, s. 548-551.
Category: Case Report

Summary

We present the case report of bilateral renal angiomyolipomas in a 70-year-old patient. Spontaneous bleeding into the retroperitoneum and hemodynamic instability required an acute surgical revision with a left-sided nephrectomy. The contralateral angiomyolipoma was selectively embolized in the second period and subsequently resected.

Keywords:

angiomyolipoma − spontaneous rupture − retroperitoneal bleeding − Wunderlich syndrome − tuberous sclerosis

Zdroje

Teplan V. a kol. Praktická nefrologie. Praha, Grada Publishing 2006:267.
Eble JN. Angiomyolipoma of kidney. Seminars in Diag Pathol. 1998;15(1):21–40.
Lamla A, Pernička J. Benigní nádory ledvin. Urologie pro Praxi 2003;3:90–93.
Wiliams RD, Dreicer R. Renal parenchymal neoplasms. In: Tanagho EA, McAninch WJ. Smiths general urology, XIX. ed., PrenticeHall Intern. Inc, 1995:372–374.
Wong K, Waters CM, Hershman MJ, et al. Angiomyolipoma of the kidney: a clinical enigma in diagnosis and management. Annals of the Royal College of Surg Of Engl. 1992:144–148.
Kawaciuk I. Nádory ledvin. In: Urologie Praha, Galén 2009:340.
Ürge T, Pitra T, Chudáček Z, et al. Nové trendy v léčbě renálního angiomyolipomu. Ces Urol. 2015;19(2):106–117.
Oon FS, Murphy M, Connolly SS. Wunderlich syndrome as the first manifestation of renal cell carcinoma. Urol J. 2010;7(2):129–132.
Stránský P, Chudáček Z, Havel V, et al. Možnosti intervenční radiologie při léčbě nádorů ledvin. Ces Urol. 2012;16(1):50–57.
Lohle PNM, Higué D, Herbreteau D. Uterine artery embolisation in women with symptomatic uterine fibroids. La Presse Médicale 2019;48(4):440–446. doi: 10.1016/j.lpm.2019.03.012.
Omodon M, Auuba G, Patel IJ. Review of renal artery embolization for treatment of renal angiomyolipoma. Clinical Nephrology and Urology Science 2016;3(1). doi: 10.7243/2054-7161-3-1.