Ileus as a complication of butterfly wing disease − case report

Česká verzia

Authors: P. Guňková ¹; D. Toman ¹; T. Posolda ²
Authors place of work: Chirurgická klinika Fakultní nemocnice Ostrava ¹; Oddělení centrálních operačních sálů Fakultní nemocnice Ostrava ²
Published in the journal: Rozhl. Chir., 2022, roč. 101, č. 2, s. 90-93.
Category: Case Report
doi: https://doi.org/10.33699/PIS.2022.101.2.90–93

Summary

Epidermolysis bullosa or butterfly wing disease is a rare genetic disorder of connective tissue associated with the formation of blisters. The clinical manifestations are very diverse and affect not only the skin cover, but also mucosal surfaces of the gastrointestinal, urogenital and respiratory systems. A large proportion of patients suffer from severe constipation with the development of megacolon. The case report describes intestinal obstruction in a patient with a dystrophic form of epidermolysis bullosa which required surgical treatment.

Keywords:

epidermolysis bullosa – bowel obstruction

Zdroje

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