The unexplainable fever syndrome in adolescence

Česká verzia

Authors: M. Kliment; P. Kertys ¹; D. Červenková ²
Authors place of work: Gynekologicko-pôrodnícka klinika, Slovenská zdravotnícka univerzita, Bratislava ; Oddelenie klinickej imunológie FN Bratislava ¹; Dermatoalergologická ambulancia, Poliklinika Ružinov, Bratislava ²
Published in the journal: Prakt Gyn 2005; 9(4): 8-10

Summary

The authors inform about the clinical syndrome, lately described and less known in gynecological community, manifested by the attacks of febrilities, often connected with abdominal symptomatology, which is standardly accompanied by increased IgD serum level. In casuistics they describe their experience with similarly progressing disease in young patient. Nowadays, they consult the case, based on existing laboratory examinations as well as the clinical course, with international working group at University in Dutch Nijmegene “International Hyper-IgD study group”, engaged in this relatively rare disease.

Key words:
unexplainable fevers in adolescence – hyperimmunoglobulinemia – mevalonate kinase enzyme deficiency – International Hyper-IgD study group

Zdroje

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