There’s no hypertrophy like hypertrophy, or don’t forget amyloidosis

Česká verzia

Authors: D. Zemánek; K. Linhartová
Authors place of work: Kardiologická klinika 2. LF UK a FN Motol Praha
Published in the journal: Kardiol Rev Int Med 2011, 13(4): 228-232

Summary

Amyloidosis is a systemic disease consisting of the depositing of proteinous substance (amyloid) in body tissues. These deposits can cause cardiac problems. A clinical picture of such an impairment can be, in the early stages of the disease, reminiscent of hypertrophic cardiomyopathy. These findings are documented in case history. Due to their fundamentally different prognosis it is important to know the difference between the two diseases. The article further includes a brief summary of the pathophysiology, diagnosis and treatment of amyloidosis, with a focus on cardiac impairment.

Keywords:
amyloidosis – hypertrophic cardiomyopathy – diagnosis – free light chains

Zdroje

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