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Desmoid fibromatosis – a rare mesenteric tumor


Authors: Grochol L. 1;  Cibulková I. 1;  Hrudka J. 2;  Hajer J. 1
Authors place of work: Divize gastroenterologie a hepatologie, Interní klinika 3. LF UK a FN Královské Vinohrady, Praha 1;  Ústav patologie 3. LF UK a FN Královské Vinohrady, Praha 2
Published in the journal: Gastroent Hepatol 2022; 76(1): 67-71
Category:
doi: https://doi.org/10.48095/ccgh202267

Summary

 In the following report, we present the case of a 31-year-old patient examined for a suspected small bowel tumour. Small bowel tumours are relatively rare and definitive diagnosis is often preceded by surgical resection. The same was true for our patient examined for a soft tissue lesion found with imaging techniques in close proximity to the small intestine. After ruling out hormonal activity, diagnostic laparotomy was performed. Desmoid fibromatosis, a rare tumour of the mesentery, was confirmed histopathologically. Although without metastatic potential, desmoid fibromatosis is a tumour with moderately malignant potential for aggressive growth into surrounding structures and organs and a large percentage of local recurrences.

Keywords:

desmoid fibromatosis – small intestine tumours – mesentery – sarcoma


Zdroje

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Štítky
Paediatric gastroenterology Gastroenterology and hepatology Surgery

Článok vyšiel v časopise

Gastroenterology and Hepatology

Číslo 1

2022 Číslo 1
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