Cricopharyngeal achalasia, a rare cause of chronic irritable cough in infant

Česká verzia

Authors: A. Jovankovičová ¹; J. Jakubíková ¹; J. Bibza ²
Authors place of work: Detská ORL klinika LFUK a DFNsP, Bratislava prednostka prof. MUDr. J. Jakubíková, CSc. ¹; Klinika detskej chirurgie LFUK a DFNsP, Bratislava prednosta MUDr. J. Trnka, CSc. ²
Published in the journal: Čes-slov Pediat 2011; 66 (2): 99-102.
Category: Kazuistika

Summary

Cricopharyngeal achalasia is a rare clinical diagnosis characterized by impaired relaxation of the upper esophageal sphincter (cricopharyngeal muscle) during deglutination. We report about 7-month old girl with a history of permanent dry irritable cough lasting several months, which was unsuccessfully treated with repeated antibiotic therapy. Esophagography and subsequent endoscopy of the esophagus and trachea under general anesthesia revealed the cause of the difficulties.

Purpose of this case report is to draw attention to the less frequent cause of recurrent inflammation of the lower respiratory tract and dysphagia in children as well as to demonstrate the suitability of esophagography in determination of the correct diagnosis.

Key words:
cricopharyngeal achalasia, irritable cough, dysphagia, esophagography

Zdroje

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