Mesenterial fibromatosis as the cause of an acute abdominal condition

Česká verzia

Authors: P. Kružliak ¹; D. Mištuna ²; K. Macháleková ³
Authors place of work: Interné odd. NsP Zvolen, Vaše zdravie, n. o. ¹; Chirurgická klinika Jesseniovej lekárskej fakulty UK a Martinskej fakultnej nemocnice, Martin ²; Ústav patologickej anatómie Jesseniovej lekárskej fakulty UK a Martinskej fakultnej nemocnice, Martin ³
Published in the journal: Gastroent Hepatol 2012; 66(4): 276-279
Category: Clinical and Experimental Gastroenterology: Case Report

Summary

Intra-abdominal fibromatosis is a locally aggressive though non-metastatic proliferation of fibrous tissue. It is a benign tumour which is mostly located on the abdominal wall, mesentery or in the retroperitoneal space. It is associated with Gardner’s syndrome or occurs sporadically. Intra-abdominal fibromatosis often leads to problems in the differential diagnosis of myofibroblastic and gastrointestinal stromal tumours, which are however characterized by much more aggressive biological behaviour and metastatic pattern. The authors described the case of an 82-year old man operated for diffuse peritonitis due to perforation of the small intestine based on mesenterial fibromatosis infiltrating the small intestine and the abdominal wall.

Key words:
mesenterial fibromatosis – Gardner’s syndrome – gastrointestinal stromal tumours (GISTs) – immunohistochemical investigation

The authors declare they have no potential conflicts of interest concerning drugs, products, or services used in the study.

The Editorial Board declares that the manuscript met the ICMJE „uniform requirements“ for biomedical papers.

Submitted:
20. 7. 2011

Accepted:
20. 9. 2011

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