A rare cause of increased abdominal size

Česká verzia

Authors: K. Dvořák ¹; J. Fulík ²
Authors place of work: Oddělení gastroenterologie a hepatologie, Krajská nemocnice Liberec, a. s., Nemocnice Liberec ¹; Chirurgická klinika 1. LF UK a IPVZ Nemocnice Na Bulovce, Praha ²
Published in the journal: Gastroent Hepatol 2018; 72(2): 119-121
Category: Hepatologie: kazuistika
doi: https://doi.org/10.14735/amgh2018119

Summary

We present a patient with an increased abdominal size and epigastric pain. Pseudomyxoma peritonei was diagnosed based on imaging studies. This is a rare clinical condition characterized by diffuse gelatinous collections in the abdomen and pelvis that are associated with mucinous implants on surfaces in the peritoneal cavity. It is caused by cystadenoma of the appendix, which leads to peritoneal seeding of mucus-producing cells. Mucins fill the peritoneal cavity. This condition has an indolent but progressive course and is fatal if untreated. The treatment of choice is radical surgical cytoreduction and heated intraperitoneal chemotherapy, which may have curative potential.

Key words:
pseudomyxoma peritonei – cystadenoma of the appendix – cytoreduction – HIPEC

The authors declare they have no potential conflicts of interest concerning drugs, products, or services used in the study.

The Editorial Board declares that the manuscript met the ICMJE „uniform requirements“ for biomedical papers.

Submitted:
26. 3. 2018

Accepted:
28. 3. 2018

Zdroje

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